罕见的口腔腺泡状横纹肌肉瘤

Alveolar Rhabdomyosarcoma of Oral Cavity – A Rare Case

　　罕见的口腔腺泡状横纹肌肉瘤

　　Rhabdomyosarcomas are the malignant tumors of the striated skeletal muscles. Rhabdomyosarcomas are the most common soft tissue sarcoma of the children, adolescents and young adults. An eleven year old boy who presented with a painless progressive lump in the floor of the mouth since 4 months which was rapidly increasing in size without any systemic symptoms or signs of any metastatic spread. A wide excision of the lump was done and histopathology was reported to be an alveolar variant of rhabdomyosarcoma. Alveolar rhabdomyosarcomas account for almost 30% of all rhabdomyosarcomas. They have predilection for deep soft tissue of the extremities. The tumor may arise at other places also though they are rare. We report a rare case of alveolar rhabdomyosarcoma occurring in the oral cavity.

　　横纹肌肉瘤是恶性横纹骨骼肌肉瘤。横纹肌肉瘤是儿童,青少年和年轻的成年人最常见的软组织肉瘤。11岁的孩子4月前发现口腔无痛肿块，肿块快速增长没有任何的症状和转移迹象。广泛切除和组织病理学发现是一个肺泡横纹肌肉瘤变异。口腔腺泡状横纹肌肉瘤占横纹肌肉瘤30%。好发于四肢深部软组织。其他地方也有发生同样也少见。我们报道发生在口腔罕见的口腔腺泡状横纹肌肉瘤。